World Summit on Oral Health and Dentistry Part II
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Accepted Abstracts

Gorlin-Goltz Syndrome: A Familial Case Report

Hugo Romero1*, Charlotte Medina Montoya2, Hernan Enrique Yanes Moya2 and Vilma Umanzor3

1Department of Oral and Maxillofacial Surgery, National Autonomous University of Honduras (UNAH), Private practice, Tegucigalpa, Honduras.
2Private practice, Tegucigalpa, Honduras.
3Department of Periodontics, National Autonomous University of Honduras (UNAH), Honduras.

Romero H, Montoya CM, Moya HEY, Umanzor V (2021) Gorlin-Goltz Syndrome: A Familial Case Report. SciTech Central Dentistry 2021.

Received: September 02, 2021         Accepted: September 07, 2021         Published: September 07, 2021


Gorlin-Goltz Syndrome (GGS) also known as Nevoid Basal Cell Carcinoma Syndrome is a rare autosomal dominant disorder. Is characterized for presenting some clinical features such as palmar pits, fused eyebrows, multiple odontogenic keratocyst, which are considered some of the most common signs. In our case, a rare familial case highlights awareness when a member of the family is diagnosed with this condition, and the probability to find in one the first degree relative. Once again it is confirmed that is impossible to determine without the radiographical analysis such as Cone Beam Computed Tomography (CBCT), ortophantomography, magnetic resonance imaging, to corroborate with clinical aspects, advising that, this could be the best way for the sake of patients benefit. Many treatments less aggressive have been proposed along the years, with a lower percentage of success against the traditional way, specifically surgical enucleation/marsupialization combined with peripheral osteotomy, in order to approach the variable behavior of nevoid basal cell carcinoma syndrome. The early diagnosis is considered the key to well manage this kind of disease, due to its aggressiveness, potential to become malignant, and in some cases, with a silent destructive pattern.
Keywords: Gorlingoltz syndrome, Odontogenic keratocyst, Palmar pits, Nevoid basal cell carcinoma syndrome