Dermatofibrosarcoma protuberans (DFSP) is commonest skin sarcoma representing less than 0.1% of all tumors. Treatment includes surgical management followed by radiotherapy to decrease chances of recurrence. We present a typical case of dermatofibrosarcoma protuberans with twice local recurrence within one year after excision. 43 years old immunocompetent married male presented to us with nodular lesion over right arm since 6 years. Patient gave the history of similar lesion over the same site in past for which he was operated twice 10 and 7 years back, respectively. Patient was advised adjuvant radiotherapy but he didn’t follow same. Since 6 years patient complained of a small raised lesion over the same site which increased gradually to the present size. Hence we report this typical case of DFSP representing its inherent tendency of recurrence.

 

Keywords: Dermatofibrosarcoma protuberans, Radiotherapy, Twice local recurrence